L carnitine is primarily synthesized in the liver from the amino acids lysine and methionine through a series of four enzymatic reactions, with the liver and kidneys converting the precursor butyrobetaine into active Mitochondrial transport of long chain fatty acids. While medium and Download Scientific Diagram Carnitine Biosynthesis Pathway L Carnitine in Mitochondria Encyclopedia MDPI Understanding the Benefits and Uses of Carnitine in Health and Fitness Fitness Health